Search on: METHYLMALONYL-COA DECARBOXYLASE 
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Descriptor English:   Methylmalonyl-CoA Decarboxylase 
Descriptor Spanish:   Metilmalonil-CoA Descarboxilasa 
Descriptor Portuguese:   Metilmalonil-CoA Descarboxilase 
Synonyms English:   Propionyl-Coenzyme A Carboxylase
Carboxylase, Propionyl-Coenzyme A
Decarboxylase, Methylmalonyl-CoA
Methylmalonyl CoA Decarboxylase
Propionyl CoA Carboxylase
Propionyl Coenzyme A Carboxylase
Propionyl-CoA Carboxylase  
Tree Number:   D08.811.520.224.125.387
Definition English:   A carboxy-lyase that catalyzes the decarboxylation of (S)-2-Methyl-3-oxopropanoyl-CoA to propanoyl-CoA. In microorganisms the reaction can be coupled to the vectorial transport of SODIUM ions across the cytoplasmic membrane. 
Entry Combination - descr/qualif English:   Methylmalonyl-CoA Decarboxylase/deficiency use Propionic Acidemia
 
See Related English:   Propionic Acidemia
 
History Note English:   2004; use METHYLMALONYL-COA DECARBOXYLASE (NM) 1980-2003 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   38186 
Unique Identifier:   D043586 

Occurrence in VHL:
 

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